Age / Sex : 58 / F

Mueller-Weiss Syndrome

Discussion

Findings:

-       Comma shape deformity of both navicular
bones

-       Diminished lateral portion of both
navicular bones

-       Medial and dorsal protusion of both
navicular bones

-       Laterally displaced bony fragment from
fracture

-       Perinavicular degenerative change

Differential Diagnosis:

Diagnosis:
 

Mueller-Weiss Syndrome

Discussion:

•       Spontaneous osteonecrosis of the
navicular bone in adults : rare

–      Koehler’s disease (in children)à is a distinct entity

•       F>M, Usually bilateral

•       damage to the blood supply of the
tarsal navicular bone

             à abnormal ossification or osteocyte
death in cartilage

•       Image findings

     - Comma shaped or hourglass shaped
navicular bone

     - Dorso-lateral
fragmentation of navicular bone

     - Wide and
lateral disaplacement of talar head

     - Perinavicular
degenerative changes

     - Cuboid sign

     - Pes planus

     - Large open
sinus tarsi

References:

Samim M,
Moukaddam HA, Smitaman E. Imaging of Mueller-Weiss Syndrome: A Review of
Clinical Presentations and Imaging Spectrum. AJR 2016; 207:W8–W18